RT Book, Section A1 Lipsker, Dan A2 Goldsmith, Lowell A. A2 Katz, Stephen I. A2 Gilchrest, Barbara A. A2 Paller, Amy S. A2 Leffell, David J. A2 Wolff, Klaus SR Print(0) ID 56080223 T1 Chapter 171. Malignant Atrophic Papulosis (Degos Disease) T2 Fitzpatrick's Dermatology in General Medicine, 8e YR 2012 FD 2012 PB The McGraw-Hill Companies PP New York, NY SN 978-0-07-166904-7 LK accessmedicine.mhmedical.com/content.aspx?aid=56080223 RD 2024/04/24 AB |PrintMalignant Atrophic Papulosis at a GlanceA rare, primary vaso-occlusive disorder, affecting mainly the skin, the gastrointestinal tract, and the central nervous system.Diagnosis relies on clinicopathologic evaluation.Characterized by numerous typical porcelain-white, atrophic papules, with a rim of rosy erythema and/or telangiectases.Pathology shows a wedge-shaped area of dermal necrosis with edema and mucin deposition.Benign forms without extracutaneous involvement are possible.