RT Book, Section A1 Comfere, Nneka I. A1 Gibson, Lawrence E. A2 Goldsmith, Lowell A. A2 Katz, Stephen I. A2 Gilchrest, Barbara A. A2 Paller, Amy S. A2 Leffell, David J. A2 Wolff, Klaus SR Print(0) ID 56078984 T1 Chapter 165. Erythema Elevatum Diutinum T2 Fitzpatrick's Dermatology in General Medicine, 8e YR 2012 FD 2012 PB The McGraw-Hill Companies PP New York, NY SN 978-0-07-166904-7 LK accessmedicine.mhmedical.com/content.aspx?aid=56078984 RD 2024/04/16 AB |PrintErythema Elevatum Diutinum at a GlanceRare disease; unknown incidence.A chronic leukocytoclastic vasculitis typified by a distinctive clinical pattern.Symmetric, erythematous, violaceous, or yellow–brown papules/nodules/plaques.Most common sites of involvement are the extensor surfaces of the hands, fingers, elbows, knees, legs, and Achilles tendon. Trunk is usually spared.Co-occurring diseases include monoclonal paraproteinemias, lymphoproliferative disorders, chronic infection, autoimmune conditions, and connective tissue diseases.Pathology consists of leukocytoclastic vasculitis in early stage lesions and a granulation-tissue-like response with fibrosis in later stages.