RT Book, Section A1 Grewal, Jasmine A1 Opotowsky, Alexander R. A2 Fuster, Valentin A2 Narula, Jagat A2 Vaishnava, Prashant A2 Leon, Martin B. A2 Callans, David J. A2 Rumsfeld, John S. A2 Poppas, Athena SR Print(0) ID 1202451290 T1 Anatomical and Physiological Classification of Adult Congenital Heart Disease T2 Fuster and Hurst's The Heart, 15e YR 2022 FD 2022 PB McGraw-Hill Education PP New York, NY SN 9781264257560 LK accessmedicine.mhmedical.com/content.aspx?aid=1202451290 RD 2024/10/12 AB Chapter SummaryThis chapter describes a brief history of classification of the numerous types of congenital heart disease (CHD) lesions and the additive value of approaches (see Fuster and Hurst's Central Illustration), focusing on recent developments including the anatomic and physiologic (AP) classification and International Pediatric and Congenital Cardiac Code (IPCCC), the basis for ICD-11 codes. Historically, classification has focused on anatomy based on pathology investigations. With the advent of surgical options for CHD management in the 20th century, attention focused on distinctions relevant to available therapeutic decisions. These surgeries, and later catheter-based treatments, modify the initial CHD, often transforming the pathophysiology and long-term consequences. As more individuals survive longer with CHD, so does the need for a common language that comprehensively and concisely describes not only the underlying congenital heart lesion, but also prior medical interventions repairs and cumulative physiologic burden. Recent classifications have explored multiple dimensions to characterizing CHD. The recently proposed AP classification aims to represent CHD anatomy, along with pertinent interventions and current physiologic status. This provides useful nuance, but also adds complexity and associated challenges. Evolving clinical phenotype requires ongoing modification, but these classification efforts share a goal: to standardize and streamline communication and thereby improve outcomes.