RT Book, Section A1 Bashore, Thomas M. A1 Granger, Christopher B. A1 Jackson, Kevin P. A1 Patel, Manesh R. A2 Papadakis, Maxine A. A2 McPhee, Stephen J. A2 Rabow, Michael W. A2 McQuaid, Kenneth R. SR Print(0) ID 1184696090 T1 Inherited Arrhythmia Syndromes T2 Current Medical Diagnosis & Treatment 2022 YR 2022 FD 2022 PB McGraw-Hill Education PP New York, NY SN 9781264269389 LK accessmedicine.mhmedical.com/content.aspx?aid=1184696090 RD 2024/04/25 AB ESSENTIALS OF DIAGNOSISIncludes long QT syndrome, Brugada syndrome, arrhythmogenic RV cardiomyopathy, and catecholaminergic polymorphic ventricular tachycardia.Genetic testing for patients with suspected congenital long QT syndrome based on family history, ECG or exercise testing, or severely prolonged QT interval (> 500 msec) on serial ECGs.Patients with long QT syndrome or catecholaminergic polymorphic ventricular tachycardia should be treated long term with an oral beta-blocker (nadolol or propranolol). ICD is indicated for patients with ventricular arrhythmia or syncope despite medical treatment.