RT Book, Section
A1 Serling-Boyd, Naomi
A1 Stone, John H.
A2 Stone, John H.
SR Print(0)
ID 1180197740
T1 Primary Angiitis of the Central Nervous System
T2 Current Diagnosis & Treatment: Rheumatology, 4e
YR 2021
FD 2021
PB McGraw Hill
PP New York, NY
SN 9781259644641
LK accessmedicine.mhmedical.com/content.aspx?aid=1180197740
RD 2024/04/20
AB Central  nervous  system  (CNS)  vasculitis  comprises  a  host  of  different  underlying  diseases  that  can  cause  inflammatory  damage  of  blood  vessels  in  the  brain  and  spinal  cord.  About  half  of  the  cases  have  no  known  cause  and  no  other  systemic  manifestations  and  are  therefore  classified  as  primary  vasculitis  of  the  CNS.  The  other  half  of  the  cases  arise  in  the  setting  of  an  underlying  disorder,  often  a  systemic  rheumatologic  disease  or  (less  commonly)  an  infection.  Those  cases  are  classified  as  secondary  forms  of  CNS  vasculitis.  Primary  vasculitis  of  the  CNS,  the  focus  of  this  chapter,  has  been  referred  to  by  many  names,  leading  to  sometimes  confusing  terminology.  We  will  use  the  term  “primary  angiitis  of  the  CNS”  (PACNS)  in  this  chapter.