RT Book, Section
A1 Hardin, J. Matthew
A2 Knoop, Kevin J.
A2 Stack, Lawrence B.
A2 Storrow, Alan B.
A2 Thurman, R. Jason
SR Print(0)
ID 1181044200
T1 Porphyria Cutanea Tarda
T2 The Atlas of Emergency Medicine, 5e
YR 2021
FD 2021
PB McGraw-Hill
PP New York, NY
SN 9781260134940
LK accessmedicine.mhmedical.com/content.aspx?aid=1181044200
RD 2024/04/23
AB Porphyrias  are  associated  with  enzymatic  defects  in  heme  biosynthesis.  Porphyria  cutanea  tarda  (PCT)  is  the  most  common  type.  Patients  have  photosensitivity,  skin  fragility,  and  characteristic  lesions  on  sun-exposed  sites  (most  common  on  the  dorsal  hands  and  forearms).  Typically,  the  skin  is  easily  traumatized  with  blisters,  erosions,  superficial  scars,  milia,  and  hypertrichosis.  PCT  does  not  cause  the  life-threatening  neurologic  attacks  associated  with  the  acute  porphyrias.