RT Book, Section A1 Lipsker, Dan A2 Kang, Sewon A2 Amagai, Masayuki A2 Bruckner, Anna L. A2 Enk, Alexander H. A2 Margolis, David J. A2 McMichael, Amy J. A2 Orringer, Jeffrey S. SR Print(0) ID 1161350431 T1 Malignant Atrophic Papulosis (Degos Disease) T2 Fitzpatrick's Dermatology, 9e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9780071837798 LK accessmedicine.mhmedical.com/content.aspx?aid=1161350431 RD 2024/10/15 AB AT-A-GLANCEMalignant atrophic papulosis (Degos disease) is a rare, primary vasoocclusive disorder, affecting mainly the skin, the GI tract, and the CNS.Diagnosis relies on clinical and pathologic evaluation and correlation.Characterized by numerous, typical, porcelain-white, atrophic papules, with a rim of rosy erythema and/or telangiectasia.Pathology shows a wedge-shaped area of dermal necrosis with edema and mucin deposition.Benign forms without extracutaneous involvement are possible.