RT Book, Section
A1 Neumann, Hartmut P. H.
A2 Jameson, J. Larry
A2 Fauci, Anthony S.
A2 Kasper, Dennis L.
A2 Hauser, Stephen L.
A2 Longo, Dan L.
A2 Loscalzo, Joseph
SR Print(0)
ID 1183992270
T1 Pheochromocytoma
T2 Harrison's Principles of Internal Medicine, 20e
YR 2018
FD 2018
PB McGraw-Hill Education
PP New York, NY
SN 9781259644016
LK accessmedicine.mhmedical.com/content.aspx?aid=1183992270
RD 2024/04/19
AB Pheochromocytomas  and  paragangliomas  are  catecholamine-producing  tumors  derived  from  the  sympathetic  or  parasympathetic  nervous  system.  These  tumors  may  arise  sporadically  or  be  inherited  as  features  of  multiple  endocrine  neoplasia  type  2  (MEN  2),  von  Hippel–Lindau  (VHL)  disease,  or  several  other  pheochromocytoma-associated  syndromes.  The  diagnosis  of  pheochromocytomas  identifies  a  potentially  correctable  cause  of  hypertension,  and  their  removal  can  prevent  hypertensive  crises  that  can  be  lethal.  The  clinical  presentation  is  variable,  ranging  from  an  adrenal  incidentaloma  to  a  hypertensive  crisis  with  associated  cerebrovascular  or  cardiac  complications.