TY - CHAP M1 - Book, Section TI - Chapter 166. Adamantiades–Behçet Disease A1 - Zouboulis, Christos C. A2 - Goldsmith, Lowell A. A2 - Katz, Stephen I. A2 - Gilchrest, Barbara A. A2 - Paller, Amy S. A2 - Leffell, David J. A2 - Wolff, Klaus PY - 2012 T2 - Fitzpatrick's Dermatology in General Medicine, 8e AB - |PrintAdamantiades–Behçet Disease at a GlanceRare disease with worldwide distribution but strongly varying prevalence; certain ethnic groups are mainly affected.A genetically determined disorder with a probable environmental triggering factor.Multisystem occurrence, with oral aphthous ulcers, genital ulcers, papulopustules, erythema nodosum-like lesions, uveitis, and arthropathy as most common signs.Inflammatory disease representing a neutrophilic vascular reaction or vasculitis.Chronic relapsing progressive course and potentially poor prognosis (especially in males with systemic presenting signs; mortality, 0–6%). SN - PB - The McGraw-Hill Companies CY - New York, NY Y2 - 2024/04/19 UR - accessmedicine.mhmedical.com/content.aspx?aid=56079113 ER -