TY - CHAP M1 - Book, Section TI - Adamantiades–Behçet Disease A1 - Zouboulis, Christos C. A2 - Kang, Sewon A2 - Amagai, Masayuki A2 - Bruckner, Anna L. A2 - Enk, Alexander H. A2 - Margolis, David J. A2 - McMichael, Amy J. A2 - Orringer, Jeffrey S. PY - 2019 T2 - Fitzpatrick's Dermatology, 9e AB - AT-A-GLANCERare disease with worldwide distribution but strongly varying prevalence; certain ethnic groups are mainly affected.A genetically determined disorder with a probable environmental triggering factor.Multisystem occurrence, with oral aphthous ulcers, genital ulcers, papulopustules, erythema nodosum–like lesions, uveitis, and arthropathy as the most common signs.Inflammatory disease representing a neutrophilic vascular reaction or vasculitis.Chronic, relapsing, and progressive course with a potentially poor prognosis (especially in males with systemic presenting signs; mortality, 0%-6%). SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accessmedicine.mhmedical.com/content.aspx?aid=1161350001 ER -