TY - CHAP M1 - Book, Section TI - Primary Angiitis of the Central Nervous System A1 - Serling-Boyd, Naomi A1 - Stone, John H. A2 - Stone, John H. Y1 - 2021 N1 - T2 - Current Diagnosis & Treatment: Rheumatology, 4e AB - Central nervous system (CNS) vasculitis comprises a host of different underlying diseases that can cause inflammatory damage of blood vessels in the brain and spinal cord. About half of the cases have no known cause and no other systemic manifestations and are therefore classified as primary vasculitis of the CNS. The other half of the cases arise in the setting of an underlying disorder, often a systemic rheumatologic disease or (less commonly) an infection. Those cases are classified as secondary forms of CNS vasculitis. Primary vasculitis of the CNS, the focus of this chapter, has been referred to by many names, leading to sometimes confusing terminology. We will use the term “primary angiitis of the CNS” (PACNS) in this chapter. SN - PB - McGraw Hill CY - New York, NY Y2 - 2024/03/28 UR - accessmedicine.mhmedical.com/content.aspx?aid=1180197740 ER -