TY - CHAP M1 - Book, Section TI - Idiopathic Pulmonary Fibrosis A1 - Tighe, Robert M. A1 - Meltzer, Eric B. A1 - Noble, Paul W. A2 - Grippi, Michael A. A2 - Elias, Jack A. A2 - Fishman, Jay A. A2 - Kotloff, Robert M. A2 - Pack, Allan I. A2 - Senior, Robert M. A2 - Siegel, Mark D. PY - 2015 T2 - Fishman's Pulmonary Diseases and Disorders, 5e AB - In simplest terms, pulmonary fibrosis equates with the growth of “scar” in the lung. Scarred lung can assume any one of a variety of patterns; these patterns define unique pathologic phenotypes. When scar assumes a patchy distribution and appears to emanate from the pleural surface, it is recognized as the “usual” type—otherwise known as usual interstitial pneumonia (UIP). The disease in which UIP manifests without cause or trigger is called idiopathic pulmonary fibrosis (IPF). IPF is, therefore, a type of pulmonary fibrosis (also known as interstitial lung disease [ILD]). IPF is recognized by a unique compilation of clinical, radiographic, and pathologic features. IPF causes breathlessness, disability due to respiratory insufficiency and, in most instances, eventually leads to death. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/29 UR - accessmedicine.mhmedical.com/content.aspx?aid=1122360789 ER -