TY - CHAP M1 - Book, Section TI - Malignant Atrophic Papulosis (Degos Disease) A1 - Lipsker, Dan A2 - Kang, Sewon A2 - Amagai, Masayuki A2 - Bruckner, Anna L. A2 - Enk, Alexander H. A2 - Margolis, David J. A2 - McMichael, Amy J. A2 - Orringer, Jeffrey S. PY - 2019 T2 - Fitzpatrick's Dermatology, 9e AB - AT-A-GLANCEMalignant atrophic papulosis (Degos disease) is a rare, primary vasoocclusive disorder, affecting mainly the skin, the GI tract, and the CNS.Diagnosis relies on clinical and pathologic evaluation and correlation.Characterized by numerous, typical, porcelain-white, atrophic papules, with a rim of rosy erythema and/or telangiectasia.Pathology shows a wedge-shaped area of dermal necrosis with edema and mucin deposition.Benign forms without extracutaneous involvement are possible. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/10/12 UR - accessmedicine.mhmedical.com/content.aspx?aid=1161350431 ER -