I. Monocytopenia A. Aplastic anemia1 B. Hairy cell leukemia2 C. MonoMAC syndrome3,4,5,6,7 D. Glucocorticoid therapy8,9 II. Monocytosis A. Benign (1) Reactive monocytosis10 (2) Exercise-induced11 B. Clonal monocytosis Indolent (1) Chronic idiopathic monocytosis12 (2) Oligoblastic myelogenous leukemia (myelodysplasia)13 Progressive (1) Acute monocytic leukemia14,15,16 (2) Dendritic cell leukemia17,18,19 (3) Progenitor cell monocytic leukemia20 (4) Chronic myelomonocytic leukemia21,22 (5) Juvenile myelomonocytic leukemia23 III. Macrophage Deficiency A. Osteopetrosis (isolated osteoclast deficiency)24,25 IV. Inflammatory Histiocytosis (Chap. 71) A. Primary hemophagocytic lymphohistiocytosis26,27,28 (1) Familial (2) Sporadic B. Other inherited syndromes with hemophagocytosis lymphohistiocytosis: Chédiak-Higashi, X-linked lymphoproliferative, Gracelli29 C. Infectious hemophagocytic histiocytosis30,31 D. Tumor-associated hemophagocytic histiocytosis31,32 E. Drug-associated hemophagocytic histiocytosis33 F. Disease-associated hemophagocytic histiocytosis29,30,31,32 G. Juvenile rheumatoid arthritis (macrophage activation syndrome)33,34 H. Sinus histiocytosis with massive lymphadenopathy35,36 V. Storage Histiocytosis (Chap. 72) A. Gaucher disease37 B. Niemann-Pick disease38 C. Gangliosidosis39 D. Sea-blue histiocytosis syndrome40 VI. Clonal (Neoplastic) Histiocytosis (Chap. 71) A. Langerhans cell histiocytosis41,42 (1) Localized (2) Systemic B. Tumors or sarcomas of histiocytes and dendritic cells43 (1) Histiocytic sarcoma (2) Langerhans cell sarcoma (3) Interdigitating dendritic cell sarcoma (4) Follicular dendritic cell sarcoma VII. Monocyte and Macrophage Dysfunction44,45,46 A. α1-Proteinase inhibitor deficiency47,48 B. Chédiak-Higashi syndrome49 C. Chronic granulomatous disease50,51 D. Chronic lymphocytic leukemia52,53 E. Disseminated mucocutaneous candidiasis54,55 F. Glucocorticoid therapy56,57 G. Kawasaki disease58,59 H. Malakoplakia60 I. Mycobacteriosis syndrome61,62,63 J. Leprosy64 K. Posttraumatic65,66 L. Septic shock-induced67,68,69 M. Critically ill subjects70 N. Solid tumors71,72 O. Tobacco smoking73,74 P. Marijuana smoking or cocaine inhalation75,76 Q. Whipple disease77,78 R. Human interleukin (IL)-10 effects; Epstein-Barr virus IL-10–like gene product (vIL-10)79,80 VIII. Atherogenesis81,82,83,84,85 IX. Thrombogenesis85,86,87,88 X. Obesity89 XI. Aging90,91,92 |